JOURNAL OF EVIDENCE BASED MEDICINE AND HEALTHCARE

Table of Contents

2019 Month : September Volume : 6 Issue : 38 Page : 2603-2605

HYDRANENCEPHALY WITH ANTERIOR ABDOMINAL WALL DEFECT- A CASE REPORT

Ritu Saloi1, Roonmoni Deka2, Santanu Kumar Sarma3

Dr. Roonmoni Deka,
Professor and Head,
Department of Anatomy,
Tezpur Medical College, Bihaguri,
Tezpur- 784010, Assam.
E-mail: roonmonideka@gmail.com
DOI: 10.18410/jebmh/2019/536

PRESENTATION OF CASE
A 21 year old primigravida delivered a stillborn female baby with weight of 2.6 kg in the Department of Obstetrics and Gynaecology, Tezpur Medical College & Hospital, Tezpur, Assam. There was no family history of any genetic or congenital anomalies. The patient didn’t smoke and there was no history that suggested any exposure to toxins or other chemical agents. The patient did not attend the antenatal clinic regularly and had not undergone routine US scan, anomaly scan or growth scan of the foetus during pregnancy. The foetus of 35 weeks gestational age was sent to the Department of Anatomy for study of congenital anomalies after taking written consent from the parents. The foetus was immediately fixed with 10% formalin. The foetus was then examined for internal and external defects. On examination, there was almost complete absence of the cerebral hemispheres and it was replaced by a membranous sac filled with cerebrospinal fluid and necrotic debris covered by leptomeninges. There was associated anterior abdominal wall defect with evisceration of developing bowel loops and liver with no membrane covering them. The foetus was dissected to detect any underlying abnormality. On dissection the other abdominal viscera were found to be normal, but the left lung and rib cage was found to be absent.