Sujata S. Giriyan, Parvathi S. Jigalur, Anita Karani
Osteofibrous dysplasia is a rare self-limiting benign fibro-osseous lesion characteristically involving cortical bone of the anterior mid-shaft of tibia. Osteofibrous dysplasia is almost invariably diagnosed during the first decade of life, usually in the first 5 years. In our case 16 year old girl presented with gradually increasing deformity over left leg since 6 years. X ray was suggestive of fibrous cortical defect. Excised bone lesion from shaft of middle one third of left tibia showed microscopic features suggestive of osteofibrous dysplasia. This case is presented because of its rarity, as osteofibrous dysplasia accounts for only 0.2% of primary bone tumours. OFD is rare after 15 years of age and is uncommon in females. In view of the risk of association of osteofibrous dysplasia with adamantinoma, correct and timely diagnosis is necessary.
