Rajesh Kumar Gupta, Aditya Gupta
A 10 years old girl presented to us with chief complaint of increasing broadening of upper ends of both legs. There was no other complaint except that she has not lost her milk teeth completely. No positive family history was elicitable. Examination of parents & other two siblings was normal. On examination she had irregular dentition in the lower jaw. There was broadening of medial ends of both clavicles, upper ends of both humeri, lower ends of both radii, lower ends of both femurs and upper ends of both tibias. Medial ends of ribs were prominent and thickened. Measurements of the body segments revealed that lower segment was relatively longer than normal. Skeletal survey was done. There was diffuse osteoporosis. The X-ray skull showed mild thickening of the vault and there was lack of pneumatisation of frontal and maxillary sinuses
