Bharathi Mohan Matha
BACKGROUND
The incidence of Prelingual deafness with bilateral profound sensory neural hearing loss varies among different regions with overall prevalence rate of one case per 1000 live births. Overall, there are more than 40 million such children all over the World. Hearing losses may be genetic or non-genetic. Genetic hearing losses (50%) may be syndromic (15%) or non-syndromic (35%). Genetic hearing loss may be Autosomal or X-linked, Dominant or Recessive, Syndromic or Non-Syndromic. Adequate radiological assessment and confirmation of select cases is utmost important before proceeding to cochlear implant surgery.
This study aims at a statistical analysis of various radiological presentation in bilateral profound sensory neural hearing loss in prelingual deafness children selected for cochlear implant in our Institution for a period of one year from January 2016 to January 2017, with study and analysis of Michel’s Aplasia and its variations included in the study.
MATERIALS AND METHODS
The study is done as a retrospective study at Vellore Medical College at the ENT Department for a period of one year from Jan 2016- Jan 2017, based on the radiological presentation of 20 children included in the study group with other prior investigations. Interpretation was done based on the inner ear anomalies and individual variations are analysed. Study Design- Retrospective study.
RESULTS
Radiological analysis of 20 cases included in the study group of Prelingual deafness candidates with bilateral profound sensory neural hearing loss selected for cochlear implant showed that three cases had Michel’s Aplasia with individual radiological variations which were analysed, while other cases had radiologically normal middle and inner ear.
CONCLUSION
Inner ear anomalies of children with bilateral profound sensory neural hearing loss are variable. Although, incomplete partition type and cochlear Hypoplasia type are common according to International studies, Michel’s Aplasia (15%) is the most common anomaly in our study with some radiological variations.
