Annapurna Rao B1, Ajay Kumar B2, Krishna Prasad P3, Rama Koteswara Rao N4
Rhabdomyosarcoma of Maxillary sinus is a rare tumor usually occurring in children. A 30 year old adult female patient attending the ENT department of our Hospital presented with rapidly progressing tumor arising from Left maxillary sinus. It was extending into the left orbit, Nasal cavity and oropharnyx as seen in the CT scan. Histopathology and Immuno-histochemistry positive to CD-99, Desmin and Myo-D1 confirmed the diagnosis of Rhabdomyosarcoma. Five cycles of chemotherapy regimen with Vincristine, Adriamycin and Cyclophosphamide lead to complete resolution of tumor and regression of Proptosis of left eye.